Specific Types & Syndromes
Hydrocephalus in myelomeningocele
Hydrocephalus in myelomeningocele is the hydrocephalus that commonly accompanies this form of spina bifida, through its link to Chiari II malformation.
In short: Hydrocephalus in myelomeningocele
- Most children with myelomeningocele develop hydrocephalus.
- It is linked to the associated Chiari II malformation.
- It is often treated with a shunt or, in selected cases, ETV.
- It is a central part of spina bifida care.
What it is
Hydrocephalus in myelomeningocele refers to the hydrocephalus that commonly accompanies myelomeningocele (the most significant form of spina bifida). It arises largely because of the associated Chiari II malformation, which obstructs CSF flow.
Understanding Hydrocephalus in myelomeningocele
Because myelomeningocele is so often accompanied by Chiari II malformation — which displaces hindbrain structures and disrupts CSF flow and outlets — most affected children develop hydrocephalus requiring treatment. Management is typically with a shunt, though endoscopic third ventriculostomy (sometimes with choroid plexus cauterization) is considered in selected cases. Because hydrocephalus is so common in this group, children with myelomeningocele are monitored for it from early on, and its management is a central part of their comprehensive care, alongside care for the spinal defect.
Why it matters
Understanding hydrocephalus in myelomeningocele helps families see why it is so common in this form of spina bifida, through the Chiari II link, and why monitoring and treating it is integral to these children's care.
Common questions
Why is hydrocephalus common in myelomeningocele?
Through the associated Chiari II malformation that obstructs CSF flow.
How is it treated?
Often with a shunt, or in selected cases ETV.
Is it part of spina bifida care?
Yes — a central part.
Bottom line
Hydrocephalus in myelomeningocele commonly accompanies this spina bifida through Chiari II malformation and is central to care.
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