Many encephaloceles are first found before birth, during routine pregnancy imaging. Understanding how diagnosis works can make the process less bewildering.
Ultrasound: the usual first clue
Encephalocele is most often discovered on a prenatal ultrasound, sometimes as early as the late first trimester (around 11–13 weeks) but frequently during the standard second-trimester anatomy scan. On ultrasound, it may appear as a sac-like protrusion along the midline of the skull, with a visible bony defect.
Fetal MRI: the detailed picture
If ultrasound suggests an encephalocele, your team may recommend a fetal MRI. MRI gives superior soft-tissue detail and can clarify:
- The exact location and size of the defect
- Whether the sac contains only fluid and membranes, or also brain tissue
- How the rest of the brain has formed
- Whether other findings (like hydrocephalus) are present
Fetal MRI is usually performed later in pregnancy (often after about 22 weeks), partly because the fetus is larger and easier to image. This detailed information is essential for counseling and for planning delivery and surgery.
Why the blood test is often normal
Many parents are surprised that the standard maternal blood screen (alpha-fetoprotein, or AFP) is often normal with encephalocele. The reason: most encephaloceles are covered by skin or a thin membrane, so the AFP that signals "open" defects like spina bifida doesn't leak out the same way. A normal AFP does not rule out encephalocele — imaging is the key tool.
What happens after detection
After an encephalocele is identified, families are typically referred to a fetal center or children's hospital for:
- Detailed imaging and a full anatomy review
- Counseling with maternal-fetal medicine, neurosurgery, and craniofacial specialists
- Discussion of possible genetic testing
- Delivery and treatment planning
Sources
- Boston Children's Hospital — Encephaloceles (prenatal detection)
- Nationwide Children's Hospital — Encephalocele (Fetal Center)
- StatPearls (NCBI Bookshelf) — Encephalocele
- Cleveland Clinic — Encephalocele