Associated Conditions & Findings
Chiari III malformation
Chiari III malformation is a rare, severe form involving a posterior encephalocele that contains hindbrain tissue.
In short: Chiari III malformation
- It specifically involves a posterior encephalocele with cerebellar or brainstem tissue.
- It is the type most directly connected to encephalocele.
- It is assessed carefully with imaging.
- Its outlook depends on the tissue involved and associated findings.
What it is
It is a rare, severe Chiari type in which a posterior encephalocele (in the occipital or high cervical region) contains hindbrain tissue, such as cerebellum or brainstem. It is the Chiari type most directly connected to encephalocele.
Understanding Chiari III malformation
Because it involves hindbrain tissue in the encephalocele sac, imaging assesses exactly which structures are present, and the outlook depends on the tissue involved and any associated findings. The team plans repair with particular care given the important structures that may be in the sac, and discusses the specific findings with the family.
Why it matters
Understanding Chiari III helps families see why a posterior encephalocele is examined so carefully for hindbrain involvement, and why the outlook is individualized based on the specific tissue and findings.
Common questions
What is in a Chiari III encephalocele?
Hindbrain tissue such as cerebellum or brainstem.
Is it the type linked to encephalocele?
Yes — most directly.
What determines the outlook?
The tissue involved and any associated findings.
Bottom line
Chiari III malformation is a severe posterior encephalocele containing hindbrain tissue, assessed carefully with imaging.
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