Causes, Risk Factors & Associated Conditions

Spina bifida (myelomeningocele)

Spina bifida is a birth defect of the spine that, in its most significant form, is almost always associated with Chiari malformation type II.

In short: Spina bifida (myelomeningocele)

  • It is a birth defect where the spine does not close fully.
  • Its most significant form is myelomeningocele.
  • It is almost always associated with Chiari type II.
  • Chiari II management is part of spina bifida care.

What it is

Spina bifida is a birth defect in which the spine and spinal canal do not close fully during development. In its most significant form, myelomeningocele, the spinal cord and its coverings protrude through an opening in the spine — and this form is almost always associated with Chiari malformation type II.

Understanding Spina bifida (myelomeningocele)

Myelomeningocele, the most serious form of spina bifida, is intrinsically linked to Chiari II: nearly all children with myelomeningocele have the type II malformation, in which the cerebellum and brainstem are displaced downward. This connection means that Chiari II is essentially part of the spectrum of myelomeningocele, and its management — along with the commonly associated hydrocephalus — is integrated into the comprehensive care of children with spina bifida. These children are monitored for symptoms of Chiari II (such as breathing or swallowing problems), which can sometimes be serious in infancy. Understanding spina bifida and Chiari clarifies the close link between myelomeningocele and Chiari II and why their care is combined.

Why it matters

Understanding spina bifida and Chiari helps families of children with myelomeningocele see why Chiari II is part of that condition, why it is monitored from birth, and why related symptoms warrant attention.

Common questions

What is spina bifida?

A birth defect where the spine does not close fully.

How does it relate to Chiari?

Its most significant form (myelomeningocele) is almost always associated with Chiari II.

Is Chiari II part of spina bifida care?

Yes — its management is integrated into comprehensive care.

Bottom line

Spina bifida, in its most significant form (myelomeningocele), is almost always associated with Chiari II, whose management is part of spina bifida care.

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