Causes & Risk Factors
Dandy-Walker malformation
Dandy-Walker malformation is a condition affecting the cerebellum and fourth ventricle that is commonly associated with hydrocephalus.
In short: Dandy-Walker malformation
- It involves the cerebellum and the fourth ventricle.
- It often includes an enlarged fourth ventricle and a cyst at the back of the brain.
- It is commonly associated with hydrocephalus.
- It is identified on brain imaging.
What it is
Dandy-Walker malformation is a congenital condition affecting the cerebellum and the fourth ventricle. It typically involves underdevelopment of part of the cerebellum (the vermis) and an enlarged, cyst-like fourth ventricle at the back of the brain.
Understanding Dandy-Walker malformation
The malformation can disrupt the normal flow and outlets of CSF from the fourth ventricle, and it is commonly associated with hydrocephalus. The features and severity vary, and it can occur in isolation or with other brain or systemic findings. Hydrocephalus associated with Dandy-Walker malformation is managed with CSF diversion such as a shunt or, in some cases, an endoscopic procedure; the approach depends on the specific anatomy. The malformation is identified on brain imaging, which characterizes the cerebellum, the fourth ventricle, and the associated cyst.
Why it matters
Understanding Dandy-Walker malformation helps families see why this condition of the back of the brain is commonly associated with hydrocephalus, and why imaging and individualized treatment of the hydrocephalus are part of care.
Common questions
What does Dandy-Walker malformation involve?
The cerebellum and the fourth ventricle.
Is it associated with hydrocephalus?
Yes — commonly.
How is it identified?
On brain imaging.
Bottom line
Dandy-Walker malformation affects the cerebellum and fourth ventricle and is commonly associated with hydrocephalus.
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